Clinical Case Database / Category: Patient Management
Supranuclear palsy
Publication details
Dr Khaled Amar, Dr Ryan Aguiar, Dr. Jonathan Hewitt
Foundation Years Journal, volume 4, issue 3, p.19 (123Doc Education, London, March 2010)
Abstract
Progressive supranuclear palsy (PSP), also known as Steele-Richardson-Olszewski syndrome, is an uncommon neurodegenerative disease which often starts in middle and late life, and is frequently misdiagnosed as Parkinson's disease (1). PSP is characterised by a predominantly axial Parkinsonism with head retraction and a poor response to levodopa. Other classic features include an early onset of postural instability and falls together with paralysis of downward gaze. Cognitive impairment and dementia is well documented in PSP but a presentation with dementia prior to the motor features is rare. We present a case of PSP that presented with cognitive impairment progressing to a dementia picture for 4 years before the onset of the typical motor features of PSP.
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Authors
Dr Khaled Amar
Consultant Physician
Royal Bournemouth Hospital, Dorset
khaled.amar@rbch.nhs.uk
Dr Ryan Aguiar
Clinical psychologist
King's Park Unit
Bournemouth, Dorset
Dr. Jonathan Hewitt
Consultant in old age Psychiatry
Barrow Hospital, Bristol
References
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The Foundation Years Clinical Cases Database is a selection of 600 peer-reviewed clinical cases in the field of patient safety and clinical practice, specifically focused on the clinical information needs of junior doctors, based around the Foundation Year Curriculum programme (MMC). The cases have been chosen to align with the Foundation Year Curriculum.
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